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'My son has a rare condition only 15 people have' | 'My son has a rare condition only 15 people have' |
(4 days later) | |
Harrison has a rare condition which affects just 15 people in the world, his parents said | |
The parents of a five-year-old boy say they "constantly worry every day" because he has a rare condition, which means "there is always a chance of cardiac arrest". | The parents of a five-year-old boy say they "constantly worry every day" because he has a rare condition, which means "there is always a chance of cardiac arrest". |
Harrison's dad Kelham and stepmother Shannon say they were shocked when they were told their son had a condition only 15 people in the world had. | Harrison's dad Kelham and stepmother Shannon say they were shocked when they were told their son had a condition only 15 people in the world had. |
Harrison has a rare mutation in the Filamin C gene, also known as FLNC, which impacts his spine, heart and lungs. | Harrison has a rare mutation in the Filamin C gene, also known as FLNC, which impacts his spine, heart and lungs. |
The family, from Ilkeston in Derbyshire, are now fundraising for a specialist car seat to make his weekly 260-mile round trips to Great Ormond Street Hospital in London more comfortable. | |
Kelham, 30, says due to the rarity of the condition, there is not a lot of a research, and it is "difficult to know what the future holds" for his son. | Kelham, 30, says due to the rarity of the condition, there is not a lot of a research, and it is "difficult to know what the future holds" for his son. |
He noticed something was not right when he stopped one afternoon with Harrison in the car. | He noticed something was not right when he stopped one afternoon with Harrison in the car. |
Aged two at the time, Harrison began to vomit in his car seat. Arriving home five minutes later, Kelham said he noticed a curve in his back while he was changing him. | Aged two at the time, Harrison began to vomit in his car seat. Arriving home five minutes later, Kelham said he noticed a curve in his back while he was changing him. |
After taking him to A&E, medics diagnosed Harrison with scoliosis. But further examinations were later carried out, and after a number of trips to the Queen's Medical Centre in Nottingham, Harrison took part in genetic testing. | After taking him to A&E, medics diagnosed Harrison with scoliosis. But further examinations were later carried out, and after a number of trips to the Queen's Medical Centre in Nottingham, Harrison took part in genetic testing. |
The family said the specialist car seat would improve Harrison's wellbeing | The family said the specialist car seat would improve Harrison's wellbeing |
"There was nothing to suggest something was wrong when he was born and was just a normal little boy," added Kelham. | "There was nothing to suggest something was wrong when he was born and was just a normal little boy," added Kelham. |
"The hospital tests came back as a gene mutation called FLNC (Filamin C); it's very rare, and 15 people in the world have what he has. We were really shocked when we were told." | "The hospital tests came back as a gene mutation called FLNC (Filamin C); it's very rare, and 15 people in the world have what he has. We were really shocked when we were told." |
The condition has led to Harrison developing a curved bend in his spine, so his shoulders and the bottom of his back are no longer in line. | The condition has led to Harrison developing a curved bend in his spine, so his shoulders and the bottom of his back are no longer in line. |
In turn, this has meant Harrison is at higher risk of further complications. | In turn, this has meant Harrison is at higher risk of further complications. |
Harrison has restrictive cardiomyopathy - a heart muscle disease where the heart muscle becomes stiff, preventing it from relaxing and filling with blood properly. | Harrison has restrictive cardiomyopathy - a heart muscle disease where the heart muscle becomes stiff, preventing it from relaxing and filling with blood properly. |
The scoliosis also puts pressure on the lungs and has decreased his respiratory function, causing lung disease. | The scoliosis also puts pressure on the lungs and has decreased his respiratory function, causing lung disease. |
The family said Harrison now faced an arduous surgery to remove vertebrae and have metal rods fused to his spine to straighten it, after wearing a halo device fixed to his skull and leg bones to slowly pull his spine into a straighter position. | The family said Harrison now faced an arduous surgery to remove vertebrae and have metal rods fused to his spine to straighten it, after wearing a halo device fixed to his skull and leg bones to slowly pull his spine into a straighter position. |
Dad Kelham said the family were shocked when they were told about the condition | Dad Kelham said the family were shocked when they were told about the condition |
"It's a struggle in day-to-day life, because there's not a lot of information about the condition, there isn't a lot of research we can look at," Kelham said. | "It's a struggle in day-to-day life, because there's not a lot of information about the condition, there isn't a lot of research we can look at," Kelham said. |
"We both constantly worry every day because with FNLC there's always a chance of cardiac arrest. | "We both constantly worry every day because with FNLC there's always a chance of cardiac arrest. |
"We don't want that to happen, so we take every day as it comes, and put a smile on Harrison's face and we do the best we can as parents. | "We don't want that to happen, so we take every day as it comes, and put a smile on Harrison's face and we do the best we can as parents. |
"But Harrison doesn't stop doing what he does, and we keep going." | "But Harrison doesn't stop doing what he does, and we keep going." |
Due to his condition, Kelham and Shannon, 31, have to take Harrison to Great Ormond Street Hospital in London for treatment - something the family struggle with. | |
"His current car seat isn't right for him, he gets agitated trying to get comfortable, and we have to keep stopping every 30 to 45 minutes," Kelham added. | "His current car seat isn't right for him, he gets agitated trying to get comfortable, and we have to keep stopping every 30 to 45 minutes," Kelham added. |
"Car journeys are a problem in general, and he works himself up and can be sick because of it." | "Car journeys are a problem in general, and he works himself up and can be sick because of it." |
Harrison attends Great Ormond Street Hospital up to four times a month for specialist treatment | Harrison attends Great Ormond Street Hospital up to four times a month for specialist treatment |
The family have partnered up with children's disability charity Newlife in raising money for a specialist car seat moulded in the curve of his spine. | The family have partnered up with children's disability charity Newlife in raising money for a specialist car seat moulded in the curve of his spine. |
This would enable Harrison to have comfortable journeys and give the family more confidence in having more trips out with the rest of the children. | This would enable Harrison to have comfortable journeys and give the family more confidence in having more trips out with the rest of the children. |
Shannon said despite his condition, Harrison still lived life to the fullest. | Shannon said despite his condition, Harrison still lived life to the fullest. |
"He will try his best in everything that he does, like what any other child does," she said. | |
"Harrison has his challenges, but he's a happy little boy, and we love him for who he is." | "Harrison has his challenges, but he's a happy little boy, and we love him for who he is." |
Follow BBC Derby on Facebook, on X, or on Instagram. Send your story ideas to eastmidsnews@bbc.co.uk or via WhatsApp on 0808 100 2210. | Follow BBC Derby on Facebook, on X, or on Instagram. Send your story ideas to eastmidsnews@bbc.co.uk or via WhatsApp on 0808 100 2210. |
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